Cleft palate and congenital alveolar synechia syndrome.

Kim, Suk Wha; Ban, Jun Sub

Original Article

Journal of the Korean Society of Plastic and Reconstructive Surgeons 1998;25(1):60-66.
Published online January 1, 1998.

Cleft palate and congenital alveolar synechia syndrome.

Suk Wha Kim, Jun Sub Ban

Division of Pediatric Plastic Surgery, Seoul National University Children's Hospital, Seoul, Korea.

Abstract

Alveolar synechia or syngnathia is a rare anomaly showing soft tissue or bony adhesions between the alveolar ridges of maxilla and mandible. In our review of the world literature, we have identified 68 reports of alvelolar synechia. Most cases describe cleft palate and the term cleft palate and congenital alveolar synechia syndrome was coined by Verdi and 0'neal(1983). Additional anomalies such as cleft lip, micrognathia, microglossia, lower lip pits, ankyloblepharon, and limb anomalies are associated. Related syndromes may include popliteal pterygium syndrome, van der Woude syndrome, and orofaciodigital syndrome. We present a child with congenital alveolar synechia and left unilateral complete cleft lip and palate. The child had difficulty in mouth opening with a maximal anterior jaw opening of 4 mm. The fibrous synechia was resected at the age of 4 months. On dividing the fibrous band, the jaws were distracted to an opening of only 7 mm using finger dilatation. However, the maximal anterior jaw opening by passive dilatation had increased to 19.0 mm after 2 months and up to 23.1 mm after 6 months by stretching exercise of the mandible, so the child could open his mouth successfully.

Keywords: Alveolar synechia; Cleft lip and palate; Cleft palate congenital alveolar synechia syndrome