Mazabraud's Syndrome: A case report.

Hong, Jeong Geun; Lim, Jin Soo; Kwon, Ho; Chung, Sang Hoon

Case Report

Journal of the Korean Society of Plastic and Reconstructive Surgeons 2000;27(2):176-178.
Published online March 1, 2000.

Mazabraud's Syndrome: A case report.

Jeong Geun Hong, Jin Soo Lim, Ho Kwon, Sang Hoon Chung

Department of Plastic Surgery, College of Medicine, The Catholic University of Korea.

Abstract

Mazabraud's syndrome is rare benign disease characterized by the association of intramuscular myxoma and fibrous dysplasia of bone. We present a case of multiple intramuscular myxomas of the right forearm with polyostotic fibrous dysplasia. X-rays suggested fibrous dysplasia of adjacent bones and CT scans showed two intramuscular cystic masses on the right forearm. 99mTc bone scintigraphy also showed a markedly increased uptake in the skull, both scapulas, both clavicles and both humeri. The masses were successfully removed. Fibrous dysplasia of the radius and myxoma were confirmed by pathologic study.

Keywords: Mazabrauds syndrome; Fibrous dysplasia; Intramuscular myxoma