A Case Report: Surgical Treatment of Pachydermodactyly .

Rhee, Se Whan; Ahn, Hee Chang; Hwang, Weon Jung; Oh, Jung Keun; Lee, Chang Woo

Case Report

Journal of the Korean Society of Plastic and Reconstructive Surgeons 2006;33(1):124-126.
Published online January 1, 2006.

A Case Report: Surgical Treatment of Pachydermodactyly .

Se Whan Rhee, Hee Chang Ahn, Weon Jung Hwang, Jung Keun Oh, Chang Woo Lee

¹Department of Plastic and Reconstructive Surgery, College of Medicine, Hanyang University, Seoul, Korea. ahnhc@hanyang.ac.kr
²Department of Dermatology, College of Medicine, Hanyang University, Seoul, Korea.

Abstract

Pachydermodactyly is a rare distinct form of fibromatosis characterized by acquired, asymptomatic dense fibrosis and fibroblastic proliferation around one or more proximal interphalangeal joints. Intralesional triamcinolone injection may be helpful in improving the clinical appearance. A 20-year-old unemployed female patient gave a four years history of progressive swelling of the fingers affecting predominantly the proximal interphalangeal joints of index fingers of left hand and index, middle fingers of right hand. There was no pain and tenderness. Physical examination, complete blood count, antinuclear antibody, rheumatoid factor were unremarkable and radiograph of both hands showed soft tissue swelling only without bony abnormality. We excised the redundant soft tissue from the both sides of proximal interphalangeal joint with longitudinal elliptical fashion. After operation, the fingers of the patient showed marked improvement cosmetically. There were no motor or sensory changes. Pachydermodactyly was first reported in 1996 in Korea. Histologic features include an increased dermal accumulation of collagen and occasionally an increased number of fibroblast. We report for one patient with pachydermodactyly treated with longitudinal elliptical excision and obtained an improvement of clinical appearance.

Keywords: Pachydermodactyly