A Case Report of Synovial Sarcoma of the Face.

Heo, Jung; Lee, Keun Cheol; Park, Jung Min; Kim, Seok Kwun; Roh, Mee Sook; Lee, Jin Hwa

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Case Report

Journal of the Korean Society of Plastic and Reconstructive Surgeons 2005;32(6):760-762.
Published online November 1, 2005.

A Case Report of Synovial Sarcoma of the Face.

Jung Heo, Keun Cheol Lee, Jung Min Park, Seok Kwun Kim, Mee Sook Roh, Jin Hwa Lee

¹Department of Plastic and Reconstructive Surgery, College of Medicine, Dong-A University, Busan, Korea. Heoj0313@paran.com
²Department of Pathology, College of Medicine, Dong-A University, Busan, Korea.
³Department of Diagnostic Radiology, College of Medicine, Dong-A University, Busan, Korea.

Abstract

Synovial Sarcoma is the fourth most common sarcoma, accounting for 8-10 % of all sarcomas. Synovial sarcoma is highly malignant tumor of mesenchymal origin but rarely occurres in head and neck area. Less than 100 cases of synovial sarcoma occurring in head and neck area have been reported all over the world. Pathologically, there is two type of synovial sarcoma: monophasic variant is composed of only one cell type and "classic" (biphasic) synovial sarcoma has two cellular component, a spindle cell(fibrosarcoma-like) component and a pseudoepithelioma component. Recommended treatment is wide resection with negative margins. The role of chemotherapy and radiation therapy is controversial. We experienced a 42-year-old male patient with slowly enlarging, deep seated mass on right cheek. In the first operation, we suggested that the mass maybe benign tumor. But, initial excisional biopsy specimen of the primary lesion was consistent with synovial sarcoma. The final diagnosis was monophasic synovial sarcoma which was composed of spindle cells. Radical resection was performed two months later because remnant tumor was found on follow up MRI. No further treatment was done. There were no recurrence or metastasis on follow up MRI, chest CT and whole body bone scan after 15 months. This is a report of a rare case of synovial sarcoma of the face with a literature review.

Keywords: Synovial sarcoma; Monophasic; Spindle cell

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