Mercedes Benz Pattern Craniosynostosis: A Case Report.

Ryoo, Suktae; Lim, So Young; Mun, Goo Hyun

Case Report

Journal of the Korean Society of Plastic and Reconstructive Surgeons 2011;38(5):683-686.
Published online September 1, 2011.

Mercedes Benz Pattern Craniosynostosis: A Case Report.

Suktae Ryoo, So Young Lim, Goo Hyun Mun

Department of Plastic Surgery, Samsung Medical Center, Sungkyunkwan University, School of Medicine, Seoul, Korea. sy72.lim@samsung.com

Abstract

PURPOSE
Craniosynostosis of three or more cranial sutures was not common. "Mercedes Benz pattern," named by Moore1 was a rare form of craniosynostosis and had an atypical pattern of premature closure of cranial suture. It was not reported in Republic of Korea. We report this case with literature review. METHODS: A 13-months-old male patient visited our clinic due to exophthalmos. He showed normal developmental course. Other neurological tests were normal but he was Crouzon syndrome patient. CT scans showed bilateral lambdoid and posterior sagittal sutures were fused and the length of the skull was extended. Cranioplasty with pi craniotomy & Barrel-Stave osteotomy and recombination of the bone flap was performed.
RESULTS
The patient was discharged after post operative 10 days without any complications. In follow up visit after 2.7 years, he was in good state without recurrence and functional abnormality of skull.
CONCLUSION
This was the first case of Mercedes Benz pattern craniosynostosis with Crouzon syndrome in Korea. This type of craniosynostosis has to be considered differently from single type of craniosynostosis or typical syndromic craniosynostosis clinically and surgically.

Keywords: Mercedes Benz pattern; Multiple craniosynostosis; Syndromic craniosynostosis