Correction of Frontal Bone Defect in Cleidocranial Dysostosis with Porous Polyethylene(Medpor(R)): A Case Report.

Moh, Jae Seong; Na, Young Cheon

Case Report

Journal of the Korean Society of Plastic and Reconstructive Surgeons 2009;36(4):481-484.
Published online July 1, 2009.

Correction of Frontal Bone Defect in Cleidocranial Dysostosis with Porous Polyethylene(Medpor(R)): A Case Report.

Department of Plastic & Reconstructive Surgery, Wonkwang University School of Medicine, Iksan, Jeollabuk-do, Korea. ycnadr@hanmail.net

Abstract

PURPOSE
Cleidocranial dysostosis is a rare hereditary disorder affecting bones that develop by intramembranous formation. The typical features include excessive growth of transverse diameter of the skull, hypoplastic clavicles, low height and characteristic facial features. METHODS: A 28-year-old female patient visited by frontal area depression. The diagnosis was performed by computed tomographic study and radiographic imaging. The patient had widely opened anterior fontanelle, partial fused metopic suture, multiple wormian bone and supernumenary impacted teeth. Under the coronal incision, we exposed depressed frontal area and corrected with Medpor block carving.
RESULTS
Postoperatively frontoparietal skull was aestheticlly improved and satisfied the patient.
CONCLUSION
Authors report a case of cleiodocranial dysostosis who underwent correction of abnormal skull shape by Medpor(R) insertion.

Keywords: Cleidocranial dysostosis; Medpor(R)