An Unusual Cutaneous and Systemic Variant of Juvenile Xanthogranuloma.

Kim, Johng Jin; Moon, Ji Hyun; Lee, Nae Ho; Yang, Kyung Moo

Case Report

Journal of the Korean Society of Plastic and Reconstructive Surgeons 2002;29(5):478-481.
Published online September 1, 2002.

An Unusual Cutaneous and Systemic Variant of Juvenile Xanthogranuloma.

Johng Jin Kim, Ji Hyun Moon, Nae Ho Lee, Kyung Moo Yang

Department of Plastic and Reconstructive Surgery, College of Medicine, Chonbuk National University, Chonju, Korea. psjjkim@hanmail.net

Abstract

This is a case report of juvenile xanthogranulomas which developed at cutaneous lesions are rare and characterized by asymptomatic multiple cutaneous lesions and extracutaneous lesions. Juvenile xanthogranulomas are benign, usually asymptomatic, self healing yellowish papules and nodules composed of histiocytic cells that predominantly occur in infancy and childhood. Papules or nodules occur in the skin, eyes, and viscera. Juvenile xanthogranuloma is characterized histologically by a dense, sheetlike, well-demarcated histiocytic infiltration within the papillary and reticular dermis, with occasional extension into subcutaneous tissue, fascia, and peripheral muscle. We report a case of juvenile xanthogranuloma developed in a 3-months- old male infant which showed mulitiple cutaneous lesions and viscera involved the lung, heart, liver, pancreas, and testicle.

Keywords: Juvenile xanthogranuloma; Extracutaneous leseions