Orthognathic Surgery in a Patient with Factor VII Deficiency.

Baek, Rong Min; Oh, Myung June; Lee, Sang Woo

Case Report

Journal of the Korean Society of Plastic and Reconstructive Surgeons 2009;36(1):93-95.
Published online January 1, 2009.

Orthognathic Surgery in a Patient with Factor VII Deficiency.

Rong Min Baek, Myung June Oh, Sang Woo Lee

Department of Plastic Surgery Seoul National University Bundang Hospital, Seongnam, Korea. sangwoolee7@naver.com

Abstract

PURPOSE
Congenital factor VII(FVII) deficiency is a rare bleeding disorder and surgery can cause excessive bleeding due to an extrinsic pathway problem. It can be diagnosed by increased PT and decreased FVII level in coagulation test. Symptom varies according to the level of FVII, but it is essential to prevent intraoperative excessive bleeding. METHODS: In this report, we described the orthognatic surgery experience in a mandibular prognathism patient with congenital F'VII deficiency, in which recombinant activated factor VII(rFVIIa) was used to manage the bleeding. Rsults: We could get a successful result without any complication and there was minimal intraoperative bleeding.
CONCLUSION
The orthognathic surgery could therefore be safely performed in patients with congenital factor VII deficiency using rFVIIa.